Recurrent pneumonias and bronchiectasis associated a commom variable immunodeficiency
نویسندگان
چکیده
منابع مشابه
Recurrent pneumonias and bronchiectasis associated a commom variable immunodeficiency
Introduction Commom variable immunodeficiency (CVI) is the second more comom cause of Immunodeficiency. Its prevalence is about 10 000 a 50 000 persons. Its incidente is about the first and second life’s decade. Both genders are commited and it can be associated a several phenotypes such a recurrent inlfections,autoimmunity,enteropathy,neoplasms,polyclonal lymphocytic infiltration. The main rec...
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Case report Boy with 13 years old diagnosed with thrombocytopenic purpura and a normal myelogram. He presented low levels of immunoglobulins (A = 7 mg / dl, M = 14,2mg / dl and G = 140 mg / dl). Immunophenotyping of lymphocytes was altered with CD19 = 7.9% (81cells / mm3); CD4 = 56.5% (574cells / mm3) and CD8 = 12.3% (125cells / mm3). The research of vaccine antibodies (tetanus, mumps) was nega...
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Primary immunodeficiencies (PIDs) are characterized by impairment of one or more arms of the immune response, resulting in decreased defense, an increased number of infections, and, in certain cases, a higher incidence of autoimmune diseases and cancers.(1) Although PIDs are considered rare diseases, many of them are more common than are those currently diagnosed with the “heel prick” test. The...
متن کاملSevere bronchiectasis in a patient with common variable immunodeficiency.
BACKGROUND Bronchiectasis are common in Common Variable Immunodeficiency. These patients are prone to infection, leading to progressive lung destruction and accelerated FEV1 decline. CLINICAL CASE 40 year-old man, with recurrent respiratory infections, autoimmunity and diarrhea since age 7. At 17 CVID was diagnosed and IVIgG was started. During the following years, respiratory symptoms progre...
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Primary immunodeficiencies (PID) are traditionally considered childhood diseases; however, adults account for 35% of all patients with PID. Antibody deficiencies, especially Common Variable Immunodeficiency (CVID), which have their peak incidence in adulthood, require a high suspicion index. Even though the estimated frequency of CVID is not high (1:25,000), high rates of under diagnosis and un...
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ژورنال
عنوان ژورنال: World Allergy Organization Journal
سال: 2015
ISSN: 1939-4551
DOI: 10.1186/1939-4551-8-s1-a275